Almost two decades later, gass and jallow in 1982 coined the term idiopathic uveal effusion syndrome to describe idiopathic serous detachment of the choroid, ciliary body, and retina. Serum protein profiling in persons with ocular disease. Jan 21, 20 peripheral rips have been reported to occur following uveal effusion syndrome, panuveitis, trauma and acute retinal necrosis. Uveal effusion syndrome is a rare syndrome of idiopathic exudative. Uveal effusion syndrome is a rare disease which belongs to the differential diagnosis of choroidal tumour with serous retinal detachment.
Uveal effusion and secondary angleclosure glaucoma associated. Uveal diseases genetic and rare diseases information. Apr 02, 2014 uveal effusion syndrome ues is a diagnosis of exclusion. A new approach to the surgical management of idiopathic uveal. It was characterized by the accumulation of fluid escaped from the choriocapillaries into nearby free space, resulting from compressed vortex veins due to a thickened sclera. Bilateral uveal effusion and angleclosure glaucoma. The retina is a thin layer of delicate tissue in the back of your eye, which lines. Nine days after the episode the visual acuity returned to 2020 in both eyes, the iop was mm hg in the right eye and 14 mm hg in the left eye, and the uveal effusion and ciliary body swelling had resolved completely figures 34. The surgical management of uveal effusion syndrome article pdf available in eye 1 pt 11. Mechanical stretching of the rpe secondary to choroidal swelling has been suggested as the mechanism of rips due to many choroidal effusions.
Uveal effusion syndrome and hypotony maculopathy clinical gate. Retina today differentiation of choroidal effusion from. It is by definition idiopathic but can be associated with. Fullthickness sclerotomy for uveal effusion syndrome. Uveal effusion syndrome is a rare disorder characterized by the accumulation of serous transudate in the suprauveal space resulting in ciliochoroidal thickening, ciliochoroidal detachment, and serous nonrhegmatogenous retinal detachment, especially in middleaged men. Videos should be between 48 minutes in duration videos must be supplemented by an english oral or written narration narration should explain what. Retina today management of uveal effusion syndrome. Peripheral rips have been reported to occur following uveal effusion syndrome, panuveitis, trauma and acute retinal necrosis. Spontaneous resolution of uveal effusion simulating. Pdf medical therapy for uveal effusion syndrome researchgate. Scleral hydraulic conductivity and macromolecular diffusion in patients with uveal effusion syndrome. Spontaneous resolution of uveal effusion simulating choroidal.
Mahmoud soliman video 7 surgery in uveal effusion syndrome. The surgery resulted in complete resolution of the choroidal detachment and exudative retinal detachment of the left eye. Pregnancyinduced hypertensionrelated chorioretinitis resem. Here we highlight the meticulous planning that is imperative to an uncomplicated outcome. Nanopowder definition of nanopowder by medical dictionary. A new hypothesis concerning pathogenesis and technique of surgical treatment. Almost two decades later, gass and jallow in 1982 coined the term idiopathic uveal effusion syndrome to describe idiopathic serous detachment of the choroid, ciliary. Prevalence of non syndromic rp is approximately 14,000.
Mohsen abou shousha video 6 acute retinal necrosis syndrome. Uveal effusion syndrome due to increased scleral thickness or hydrostatic causes a thickened sclera 1 nanophthalmos 2 scleritis 3 hyperopia b uveal inflammation 1 vkh 2 so 3 chronic uveitis 4 post cryo or laser c other 1 idiopathic 2 ocular hypotension 3 postop 4 cc fistula conditions where dilators not miotics are indicated. Express shunt for choroidal fluid drainage in uveal effusion. Superimposed aging and hormonal changes in the sclera and its emissary channels impair its permeability to protein and predispose the eye to vortex vein obstruction. Sep 16, 2015 vine a 1986 uveal effusion in hunters syndrome.
Videos should be between 48 minutes in duration videos must be supplemented by an english oral or written narration narration should explain what the retina doctor is doing and why. Histological studies have demonstrated disruption of collagen. It is known that idiopathic uveal effusion has a poorer prognosis than other types, and that surgery or systemic steroid therapy is not effective. The thickened sclera impairs diffusion of fluid from the suprachoroidal space. An external file that holds a picture, illustration, etc. It was characterized by the accumulation of fluid escaped from the choriocapillaries into nearby free. Sympathetic ophthalmia is associated with granulomatous inflammation of the. Uveal effusion syndrome idiophathic serous detachment of the choroid, ciliary body. If you have problems viewing pdf files, download the latest version of adobe reader.
It leads to an abnormal collection of fluid that expands the suprachoroidal space, resulting in an. Uveal effusion syndrome mimicking severe chronic posterior. Some cases appear to be dose dependent as lower doses of the inciting medication may not trigger. Choroidal findings in idiopathic uveal effusion syndrome opth. Role for rapid surgical intervention in uveal effusion. For language access assistance, contact the ncats public information officer. Jan 03, 2015 what is posterior uveal effusion syndrome pues. We report choroidal findings by means of enhanced depth imaging spectraldomain optical coherence tomography edioct in a patient with. Uveal effusion syndrome ues is a diagnosis of exclusion.
Pm combined with foveoschisis has been reported in some cases 4, 5 and has been related to gene mutation 4, 6. Idiopathic uveal effusion syndrome is a rare acquired eye disease characterized by uni or bilateral abnormal fluid accumulation within the suprachoroidal space. Choroidal findings in idiopathic uveal effusion syndrome tomomi harada, shigeki machida, takamistu fujiwara, yasunori nishida, dajiro kurosakadepartment of ophthalmology, iwate medical university school of medicine, iwate, japanpurpose. Retinitis pigmentosa orphanet journal of rare diseases. Jackson tl, hussain a, morley ams, sullivan pm, hodgetts a, elosta a, et al. However, this may arise from other intraocular surgeries and a number of conditions, including inflammatory and infectious diseases, trauma, neoplasms, drug reactions, and venous congestion. In 1986, oum9 reported subscleral sclerectomy in a case of uveal effusion syndrome in korea. Cataract surgery in a nanophthalmic eye is challenging. It was characterized by the accumulation of fluid escaped from the choriocapillaries into nearby free space, resulting from compressed vortex. The correct diagnosis is important as sclerectomy or. Druginduced uveal effusions with resultant bilateral angleclosure glaucoma and myopic shift are uncommon but have been reported with a variety of medications, most notably sulfabased medications such as topiramate. It is hypothesized that the primary underlying cause of the idiopathic uveal effusion syndrome is a congenital anomaly of the sclera, and in some cases, the vortex veins. Uveal effusion syndrome is a rare disease that largely affects middleaged male subjects.
It usually coexists with high hyperopia, glaucoma, uveal effusion syndrome, and exudative retinal detachment 2, 3. A new approach to the surgical management of idiopathic uveal effusion syndrome todd e. Antihypertension treatment alone resulted in gradual resolution of the srd. Patients present with idiopathic choroidal swelling and exudative retinal detachments without clinical findings of hypotony or inflammation. A fundus photograph shows peripheral choroidal detachment and macular folds.
Uveal effusion syndrome september 2017, november 2017, march 2018 retinitis pigmentosa case presentation march 2018 20162017 dr. Grand rounds a 53yearold woman with a severe headache. Pdf to text batch convert multiple files software please purchase personal license. The onset is spontaneous and the progression of the disease is slow, often leading to bilateral serous choroidal detachment and concomitant retinal detachment, shifting subretinal fluid and, in. Abnormal scleral findings in uveal effusion syndrome. A choroidal effusion has distinctive features on both ophthalmic examination and imaging studies that can be used to differentiate it from choroidal melanoma. Nanophthalmos preparing for the challenge sujatha v. A novel technique for choroidal fluid drainage in uveal. Carotid cavernous fistulas are abnormal communications between the cavernous sinus and the external or internal carotid arteries. Uveal effusion syndrome ues is a rare, distinct primary abnormality of the choroid or sclera.
Pues is an abnormal leakage of clear fluid under the retina, which causes symptoms of blurred vision, sometimes with distortion of straight lines. Kadambi and sripriya krishnamoorthy nanophthalmos, a rare condition, is an important cause of secondary angle closure, especially in young adults. Retinitis pigmentosa rp is an inherited retinal dystrophy caused by the loss of photoreceptors and characterized by retinal pigment deposits visible on fundus examination. To describe a new method for manag ing retinal detachment associated with idiopathic uveal effusion syndrome.
Acquired retinoschisis resolved after 23gage pars plana. Following steroid treatment there was a regression after a few months. The onset is spontaneous and the progression of the disease is slow, often leading to bilateral serous choroidal detachment and concomitant retinal detachment, shifting subretinal fluid and, in severe cases, total loss of visual acuity. Uveal effusion syndrome uveal effusion syndrome ues may be idiopathic or associated with abnormalities of choroid or sclera. We have recently encountered 2 cases in which uveal effusions have occurred after. Pdf the surgical management of uveal effusion syndrome. Uveal effusion syndrome an overview sciencedirect topics. Uveal effusion syndrome usually causes peripheral chorioretinal detachment, but posterior. This condition frequently presents as central serous retinopathy. Uveal effusion, also referred to as choroidal detachment, can occur secondary to a number of ocular conditions that result in inflammatory or hydrostatic changes, including scleritis, posterior uveitis, and hypotony after glaucoma surgery.
Evaluation of uveal effusion syndrome following trabeculectomy. Deepen your understanding of uveal effusion syndrome. Spontaneous exudative detachment of the choroid and ciliary body was first reported by schepens and brockhurst in 1963 1. C bscan ultrasonography imaging of the bullous serous choroidal. Piper bahr pigment dispersion syndrome august 2016 systemic imaging case presentation september 2016 lipemia retinalis november 2016, march 2017, may 2017, june 2017 dr. Choroidal findings in idiopathic uveal effusion syndrome.
Choroidal effusionan abnormal accumulation of fluid in the suprachoroidal spaceis a common complication of glaucoma surgery. Idiopathic uveal effusion syndrome iues is a rare disease characterized by ciliochoroidal and. To our knowledge, our case represents the first report of worsening angle closure glaucoma and choroidal detachments over an extended period of two months. The most common form of rp is a rodcone dystrophy, in which the first symptom is night blindness, followed by the progressive loss in the peripheral visual field in. It is basically a diagnosis of exclusion when all other causes are ruled out. Nov 09, 2011 choroidal findings in idiopathic uveal effusion syndrome tomomi harada, shigeki machida, takamistu fujiwara, yasunori nishida, dajiro kurosakadepartment of ophthalmology, iwate medical university school of medicine, iwate, japanpurpose. Uveal effusion syndrome is a rare entity involving the idiopathic collection of serous fluid in the suprachoroidal space. Uveal effusion syndrome ues is a rare idiopathic cause of choroidal. Pdf purposeto report a case series of three patients with bilateral uveal effusion syndrome ues, treated conservatively with oral carbonic anhydrase. The visual acuity of the nanophthalmic patient was well maintained during a 3 year followup period without treatment. Uveal diseases genetic and rare diseases information center.
Case report fullthickness sclerotomy for uveal effusion syndrome. It is speculated that compression of the vortex veins may increase. Patients present with idiopathic choroidal swelling and exudative retinal detachments without clinical findings of. Uveal effusion syndrome is a rare condition characterized by idiopathic. C, ubm after treatment for the uveal effusion demonstrating deep anterior chamber and. Although rare, closure of carotid cavernous fistulas can lead to immediate ocular complications. Bupropion hydrochloride, an aminoketone antidepressant, is a dopamine reuptake inhibitor with norepinephrine and nicotinic acetylcholine receptor antagonist actions. Scientific program sessions wednesday 1st of april, 2020 11. Choroidal effusions american academy of ophthalmology. High definition spectral domain optical coherence tomography.
Evaluation of the sclera during combined sclerectomies and sclerostomies of the left eye revealed markedly thickening sclera and a reduced number of vortex veins. A new approach to the surgical management of idiopathic. Uveal effusion syndrome idiophathic serous detachment of the. Pdf purpose the purpose of the study was to investigate the corticosteroids for uveal effusion syndrome ues.
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